NR AGRX
AU Kordek,R.
TI The diagnosis of human prion diseases
QU Folia Neuropathologica 2000; 38(4): 151-60
PT journal article; review; review, tutorial
AB Prion diseases present a wide spectrum of clinical and neuropathological features. In this review, clinical and neuropathological findings are summarized along with criteria for the diagnosis of the molecular-phenotypic subtypes of sporadic Creutzfeldt-Jakob disease (CJD), familial CJD, new variant CJD, iatrogenic CJD, Gerstmann-Sträussler-Scheinker disease, fatal familial insomnia and kuru.
ZR 59
MH Adult; Age of Onset; Aged; Amyloid/analysis/genetics; Atrophy; Brain/pathology; Cerebrospinal Fluid Proteins/analysis; Child; Cluster Analysis; Codon/genetics; Creutzfeldt-Jakob; Syndrome/diagnosis/epidemiology/genetics/pathology/transmission; Disease Outbreaks; Electroencephalography; Ethnic Groups; Europe/epidemiology; Female; Gerstmann-Sträussler-Scheinker Disease/diagnosis; Human; Iatrogenic Disease; Kuru/diagnosis; Magnetic Resonance Imaging; Male; Middle Age; New Guinea/epidemiology; Prion Diseases/classification/*diagnosis/epidemiology/genetics/pathology; Prions/classification/genetics/isolation & purification; Protein Precursors/analysis/genetics; Support, Non-U.S. Gov't; United States/epidemiology
AD Department of Pathology, Chair of Oncology, Medical University, Lodz, Poland. radekkordek@interia.pl
SP englisch
PO Polen