NR AHVS
AU Marciani,M.G.; Bernardi,G.; Sancesario,G.; Gigli,G.L.; Maschio,M.; Palmieri,G.; Schiaroli,S.
TI Rapidly progressive form of Creutzfeldt-Jakob disease without dementia: a case report.
QU International Journal of Neuroscience 1996 Feb; 84(1-4): 115-20
PT journal article
AB We describe a case of a patient with Creutzfeldt-Jakob disease (CJD) characterized by a rapid clinical course lasting one and a half months, by: presence of focal dystonic movements at onset, absence of mental deterioration in the period preceding the impairment of consciousness, ataxia, myoclonus and periodic EEG abnormalities. The autopsy confirmed subacute spongiform encephalopathy, but no evident neuronal loss was observed. An acute clinical course of CJD may explain this latter histological finding which, in turn, probably provides an explanation for the absence of intellectual impairment.
IN Ein Creutzfeldt-Jakob-Patient starb nach nur 6 Wochen mit rascher Verschlimmerung der Krankheit mit Bewegungsstörungen aber ohne deutliches Nachlassen der geistigen Fähigkeiten.
ZR 12
MH Aged; Case Report; Creutzfeldt-Jakob Syndrome/pathology/physiopathology/*psychology; Electroencephalography; Human; Male; Myoclonus/physiopathology; Thalamus/pathology
AD Clinica Neurologica, Universita degli Studi di Roma Tor Vergata, Italy.
SP englisch
PO England