NR AJYQ
AU Rice,G.P.; Paty,D.W.; Ball,M.J.; Tatham,R.; Kertesz,A.
TI Spongiform encephalopathy of long duration: a family study.
QU Canadian Journal of Neurological Sciences 1980 Aug; 7(3): 171-6
PT journal article
AB Seven members of a family succumbed to prolonged dementing illnesses. In two, those dementia lasted 10 years, spongiform encephalopathy was found at autopsy. This duration of illness has not been a feature in other instances of familial Creutzfeldt-Jakob disease.
MH Adult; Brain/*pathology; Brain Diseases/diagnosis/*genetics/pathology; Case Report; Creutzfeldt-Jakob Syndrome/genetics; Dementia/diagnosis/*genetics/pathology; Female; Human; Male; Middle Age; Syndrome
SP englisch
PO Kanada