NR ARGJ
AU Cohen,D.; Kutluay,E.; Edwards,J.; Peltier,A.; Beydoun,A.
TI Sporadic Creutzfeldt-Jakob disease presenting with nonconvulsive status epilepticus
QU Epilepsy & Behavior 2004 Oct; 5(5): 792-6
PT case reports; journal article
AB Creutzfeldt-Jakob disease (CJD) is a rare prion disease characterized by a spongiform encephalopathy in humans. Although the characteristic triad of myoclonus, dementia, and periodic EEG activity is easy to recognize, unusual manifestations of the disease may be challenging and create a diagnostic dilemma. We report a case of CJD that occurred in a 26-year-old patient who presented with a receptive (Wernicke's) aphasia secondary to nonconvulsive status epilepticus.
MH Adult; Aphasia, Wernicke/complications/psychology; Brain/pathology; Creutzfeldt-Jakob Syndrome/*complications/diagnosis/pathology; Electroencephalography; Fatal Outcome; Frontal Lobe/pathology; Humans; Magnetic Resonance Imaging; Male; Status Epilepticus/diagnosis/*etiology/pathology
AD Department of Neurology, University of Michigan Health System, UH1B300/0036 Ann Arbor, MI 48109, USA
SP englisch
PO USA