NR AUIW
AU Nakamura,M.; Ogata,M.; Matsuo,Y.; Sata,T.
TI Anesthetic management of a patient with Gerstmann-Sträussler-Scheinker syndrome (mutation of prion protein)
QU Anesthesia and Analgesia 2006 Apr; 102(4): 1285-6
PT case reports; journal article
AB Gerstmann-Sträussler-Scheinker Syndrome (GSS) is a rare, infectious syndrome related to a mutation in the prion protein. A 60-yr-old, 152-cm, 31-kg woman with GSS was scheduled for open gastrostomy. This is the first report about an anesthetic experience in a patient with GSS. We describe our experience and precautions in the anesthetic management of a GSS patient.
MH Airway Obstruction/prevention & control; Anesthesia/*methods; Equipment Contamination/prevention & control; Female; Gerstmann-Sträussler-Scheinker Disease/genetics/*surgery; Humans; Intubation, Intratracheal/instrumentation/methods; Middle Aged; Mutation/*genetics; Prions/*genetics; Research Support, Non-U.S. Gov't
AD Department of Anesthesiology, University of Occupational and Environmental Health, School of Medicine, Fukuoka, Japan.
SP englisch
PO USA