NR AVSM
AU Fogel,B.; Wu,M.; Kremen,S.; Murthy,K.; Jackson,G.; Vanek,Z.
TI Creutzfeldt-Jakob disease presenting with alien limb sign
QU Movement Disorders 2006 Jul; 21(7): 1040-2
PT case reports; journal article
AB Creutzfeldt-Jakob disease is a fatal spongiform encephalopathy, which typically presents with a rapidly progressing dementia and additional neurological findings that can be quite variable and diverse. Here we report the unusual case of a patient who presented with left alien limb sign without overt cognitive impairment and was ultimately diagnosed with pathologically confirmed Creutzfeldt-Jakob disease.
MH Cerebellum/pathology; Cerebral Cortex/pathology; Creutzfeldt-Jakob Syndrome/*diagnosis/pathology; Diagnosis, Differential; Diffusion Magnetic Resonance Imaging; Disease Progression; Dominance, Cerebral/physiology; Dystonia/diagnosis/etiology; Fatal Outcome; Female; Functional Laterality; Humans; Middle Aged; Neurologic Examination; Perceptual Disorders/*diagnosis/etiology; Prions/analysis
AD Department of Neurology, UCLA Medical Center, Los Angeles, California 90095, USA. bfogel@ucla.edu
SP englisch
PO USA